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Combination therapy of the plaque form of Weber–Christian idiopathic panniculitis

https://doi.org/10.17650/1818-8338-2012-3-4-58-61

Abstract

Panniculitides are a group of heterogenic inflammatory diseases that involve the subcutaneous fat. Treatment for panniculitides, idiopathic ones in particular, has not been conclusively developed and is generally performed empirically. The paper describes a case successfully treated with glucocorticosteroids in combination with azathioprine for the plaque form of Weber–Christian panniculitis.

About the Authors

O. N. Egorova
Research Institute of Rheumatology, Russian Academy of Medical Sciences
Russian Federation


B. S. Belov
Research Institute of Rheumatology, Russian Academy of Medical Sciences
Russian Federation


S. G. Radenska-Lopovok
Research Institute of Rheumatology, Russian Academy of Medical Sciences
Russian Federation


Ye. G. Sazhina
Research Institute of Rheumatology, Russian Academy of Medical Sciences
Russian Federation


References

1. Diaz Cascajo C., Borghi S., Weyers W. Panniculitis: definition of terms and diagnostic strategy. Am J Dermatopathol 2000;22(6):530–49.

2. Requena L., Yus E.S. Panniculitis. Part I. Mostly septal panniculitis. J Am Acad Dermatol 2001;45(2):163–83.

3. Requena L., Sanchez Yus E. Panniculitis. Part II. Mostly lobular panniculitis. J Am Acad Dermatol 2001;45(3):325–61.

4. Ter Poorten M.C., Thiers B.H. Panniculitis. Dermatol Clin 2002;20(3):421–33.

5. Вербенко Е.В. Клиника, дифференциальная диагностика и лечение спонтанного панникулита.

6. Методические рекомендации. М., 1975.

7. Kirch W., Dührsen U., Hoensch H., Ohnhaus E. Cyclophosphamide-induced remission in Weber-Christian panniculitis. Rheumatol Int 1985;5(5):239–40.

8. Szyszymar B., Gwiezdzinski Z. Treatment of recurrent panniculits febrilis nonsuppurativa with methotrexate. Przegl Dermatol 1974;61(5):623–7.

9. Hotta T., Wakamatsu Y., Matsumura N. et al. Azathioprine-induced remission in Weber-Christian disease. South Med J 1981;74(2):234–7.

10. Pongratz G., Ehrenstein B., Hartung W. et al. A patient with Pfeifer-Weber-Christian disease-successful therapy with cyclosporin A: case report. Musculoskelet Disord 2010;11:18.

11. Baskan E.B., Saricaoglu H., Tunali S., Tolunay S. Effective treatment of relapsing idiopathic nodular panniculitis (Pfeifer–Weber–Christian disease) with mycophenolate mofetil. J Dermatolog Treat

12. ;14(1):57–60.

13. Казакевич Е.В., Попов В.В., Липский В.Л., Шлаганова А.А. Случай синдрома Пфейфера-Вебера-

14. Крисчена. Клин мед 1999; 77(10):54.

15. Мешков В.В., Васютин Ю.А., Вакулин Г.В. Наблюдение панникулита Пфейфера-Вебера-Крисчена,

16. симулировавшего сепсис. Клин хир 2011;(5):67–8.


Review

For citations:


Egorova O.N., Belov B.S., Radenska-Lopovok S.G., Sazhina Ye.G. Combination therapy of the plaque form of Weber–Christian idiopathic panniculitis. The Clinician. 2012;6(3-4):58-61. (In Russ.) https://doi.org/10.17650/1818-8338-2012-3-4-58-61

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ISSN 1818-8338 (Print)
ISSN 2412-8775 (Online)